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Quintessence International
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Quintessence Int 39 (2008), No. 3     4. Feb. 2008
Quintessence Int 39 (2008), No. 3  (04.02.2008)

Page 251-256, PubMed:18618041


Odontogenic keratocyst and multiple supernumerary teeth in a patient with Ehlers-Danlos syndrome-A case report and review of the literature
Ferreira jr., Osnay / Cardoso, Camila Lopes / Capelozza, Ana Lúcia Alvares / Yaedú, Renato Yassutaka Faria / da Costa, Antonio Richieri
Ehlers-Danlos syndrome (EDS) is a hereditary disorder of the connective tissue related to collagen metabolism. Deficiency or alteration of the collagen present in the tissues results in some classic signs such as skin hyperelasticity, articular hypermobility, and vascular fragility, among others. In addition, EDS oral manifestations are rarely cited in the literature. The aim of this article is to report a rare case of a young female patient with EDS who presented supernumerary teeth and an odontogenic keratocyst. There is no report in the literature of the simultaneous occurrence of these alterations. The article further highlights the importance of EDS diagnosis in patients who need dental treatment and the due care for their assistance.

Keywords: articular hypermobility, Ehlers-Danlos syndrome, odontogenic keratocyst, skin hyperelasticity, supernumerary teeth